- Glycine C Acetyltransferase (GCAT)
- Glutaryl Coenzyme A Dehydrogenase (GCDH)
- Hydroxyacyl Coenzyme A Dehydrogenase (HADH)
- 3-Hydroxyisobutyryl Coenzyme A Hydrolase (HIBCH)
- Holocarboxylase Synthetase (HLCS)
- 3-Hydroxymethyl-3-Methylglutaryl Coenzyme A Lyase (HMGCL)
- 3-Hydroxy-3-Methylglutaryl Coenzyme A Reductase (HMGCR)
- Hydroxymethylglutaryl Coenzyme A Synthase 2, Mitochondrial (HMGCS2)
- Isovaleryl Coenzyme A Dehydrogenase (IVD)
- Methylcrotonoyl Coenzyme A Carboxylase 1 (MCCC1)
- Methylcrotonoyl Coenzyme A Carboxylase 2 (MCCC2)
- Methylmalonyl Coenzyme A Mutase (MUT)
- Propionyl Coenzyme A Carboxylase Alpha (PCCa)
- Propionyl Coenzyme A Carboxylase Beta (PCCb)
- Peroxisomal D3, D2-Enoyl Coenzyme A Isomerase (PECI)
