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Anthrax Toxin Receptor 2 (ANTXR2)

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CMG-2; CMG2; ISH; JHF; Capillary Morphogenesis Protein 2

Anthrax Toxin Receptor 2 (ANTXR2)
CCC F212
HGNC 21732
MGI 1919164
PubMed 22383261
UniProt P58335
Wiki ANTXR2
ANTXR2 isa receptor for anthrax toxin. The protein binds to collagen IV and laminin, suggesting that it may be involved in extracellular matrix adhesion. Mutations in this gene cause juvenile hyaline fibromatosis and infantile systemic hyalinosis. Multiple transcript variants encoding different isoforms have been found for this gene.
Expressed in prostate, thymus, ovary, testis, pancreas, colon, heart, kidney, lung, liver, peripheral blood leukocytes, placenta, skeletal muscle, small intestine and spleen.This autosomal recessive syndrome is similar to JHF, but has an earlier onset and a more severe course. Symptoms appear at birth or within the first months of life, with painful, swollen joint contractures, osteopenia, osteoporosis and livid red hyperpigmentation over bony prominences.

Organism species: Homo sapiens (Human)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins RPF212Hu01 Recombinant Anthrax Toxin Receptor 2 (ANTXR2) Positive Control; Immunogen; SDS-PAGE; WB.
Antibodies PAF212Hu01 Polyclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) WB,IHC
MAF212Hu21 Monoclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) WB; IHC; ICC; IP.
MAF212Hu22 Monoclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) WB; IHC; ICC; IP.
MAF212Hu23 Monoclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) WB; IHC; ICC; IP.
Assay Kits SEF212Hu ELISA Kit for Anthrax Toxin Receptor 2 (ANTXR2) Enzyme-linked immunosorbent assay for Antigen Detection.

Organism species: Mus musculus (Mouse)

CATALOG NO. PRODUCT NAME APPLICATIONS
Proteins n/a Recombinant Anthrax Toxin Receptor 2 (ANTXR2) Recombinant Protein Customized Service Offer
Antibodies n/a Monoclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) Monoclonal Antibody Customized Service Offer
n/a Polyclonal Antibody to Anthrax Toxin Receptor 2 (ANTXR2) Polyclonal Antibody Customized Service Offer
Assay Kits n/a CLIA Kit for Anthrax Toxin Receptor 2 (ANTXR2) CLIA Kit Customized Service Offer
n/a ELISA Kit for Anthrax Toxin Receptor 2 (ANTXR2) ELISA Kit Customized Service Offer
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